Maxillofacial deformities in association with Goldenhar syndrome

Abstract

Goldenhar syndrome or oculoauriculovertebral dysplasia
is a complex malformation which involves many
structures and the main characteristics are: epibulbar
dermoids, auricular appendages or fistulae, deafness,
hemifacial microsomia and vertebral anomalies. Some
anomalies in facial bone structure are also observed,
especially on the maxilla. The inheritance type of this
congenital malformation in not exactly known. Other syndromes
and malformations have been documented in
association with this disorder. The purpose of this report
was to describe the clinical characteristics and oral findings
of a patient with Goldenhar syndrome.